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KMID : 0361019960390050907
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Korean Journal of Otolaryngology - Head and Neck Surgery
1996 Volume.39 No. 5 p.907 ~ p.914
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A Case of Type 1b Immotile Cilia Syndrome
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Abstract
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The immotile cilia syndrome is defined as an inborn inborn human disorder characterized by inability of cilia to beat normally. Such cilia was associated with ultrastructural defects having specific and genetically determined abnormalities. The
cilia
with ultrastructurai defects retain some abnormal ciliary motility, so we prefer primary ciliary dyskinesia. Eariy diagnosis of the disease may be important for prevention of bronchiectasis and pulmonary insufficiency. The definitive diagnosis is
ultimately confirmed by nasal electronmicroscopic biopsy and treatment is based on appropriate drainage procedure. Prognosis is excellent.
Recently the authors experienced in a 22 year old female who had got bronchiectasis and chronic sinusitis. This patient was performed bilateral endoscopic sinus surgery. The patient was discharged with good result. (Korean J Otolaryngo1 39 : 5,
1996)
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